Undifferentiated pleomorphic sarcoma with focal myogenic differentiation mimicking left atrial myxoma

Primary cardiac tumors are very rare. Cardiac sarcomas can be detected at any age, regardless of gender. At diagnosis, these mostly symptomatic and one-third metastatic. Undifferentiated pleomorphic account for 1.7% all tumors, typically localized in the left atrium, involve mitral valve. Here we present a case atrial undifferentiated sarcoma with myogenic differentiation that clinically radiologically mimicked myxoma.